Connective tissue disease associated TMA
نویسندگان
چکیده
منابع مشابه
Connective tissue disease-associated pulmonary arterial hypertension
Although rare in its idiopathic form, pulmonary arterial hypertension (PAH) is not uncommon in association with various associated medical conditions, most notably connective tissue disease (CTD). In particular, it develops in approximately 10% of patients with systemic sclerosis and so these patients are increasingly screened to enable early detection. The response of patients with systemic sc...
متن کامل[Mixed connective tissue disease].
Mixed connective tissue disease deserves to be a distinct disease entity due to the persistent citation of this disease in the literature since the original description by Sharp in 1972, in spite of the presence of several criticisms against the independency of this disease. The characteristic features of mixed connective tissue disease are: 1) the presence of anti-U1snRNP antibody with high ti...
متن کاملMixed connective tissue disease with associated glomerulonephritis and hypocomplementaemia.
Mixed connective tissue disease is an increasingly recognized entity in which renal disease is thought to be unusual and associated hypocomplementaemia even more uncommon. A patient is described who had both these features and who also illustrates many of the characteristic features of this syndrome. The response to steroids of the systemic sclerosis component is well shown and an additional fe...
متن کاملConnective tissue disease-associated pulmonary arterial hypertension: "Beijing style".
Patients with connective tissue disease (CTD)-associated pulmonary arterial hypertension (APAH) experience poorer outcomes than those with idiopathic PAH (IPAH) [1–6]. In the USA, patients with systemic sclerosis (SSc) are most commonly affected by CTD-APAH and have the worst survival [1]. Similarly, 74% of a large cohort with CTD-APAH in the UK had SSc, and these patients had poorer survival t...
متن کاملMinimal-change nephrotic syndrome associated with mixed connective-tissue disease.
Sir, Mixed connective-tissue disease (MCTD) is a rheumato-logical disorder which has combined features of systemic lupus erythematosus, systemic sclerosis (SSc), polymyositisu dermatomyositis, and rheumatoid arthritis (RA) with anti-bodies to U 1 small nuclear ribonucleoprotein (U 1 snRNP). Although renal involvement was considered to be rare in the initial description w1x, several studies demo...
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ژورنال
عنوان ژورنال: Japanese Journal of Thrombosis and Hemostasis
سال: 2014
ISSN: 0915-7441,1880-8808
DOI: 10.2491/jjsth.25.720